Fibrous Dysplasia

-is a disorder of unknown cause in which skeletal aberrations constitute the cardinal feature.

1. Key clinical features.

   1. Café au Lait spots with a “coast of Maine” appearance, pigmentation changes

   2. Common in late childhood before puberty during skeletal growth

   3. Polystotic m/c for derormities

2. Key Radiological features

   1. Clear zone in the center with a “Ground Galss Appearance” – beveled / fine fuzzy opaque edges

   2. Stimulates blastic reaction of surrounding tissue = “Rind of Sclerosis”

   3. Can change the contour of bone (expansile), with widening of meduallary, endostal thinning and scalloping

   4. Sheperds crook deformity common

Category: Orthopedics Notes , Tumors Revision